Liver, Pancreas and Kidney – Congenital Polycystic Disease
40 year old man with slow evolution of renal insufficiency progressing to uraemia.
(Top) Kidney: The kidney is enlarged. The parenchyma is replaced by multiple variably sized, non-communicating, unilocular cysts with thin walls and clean, smooth inner surfaces. Residual parenchyma is discernible.
(Centre) Liver: The non-cirrhotic liver is irregularly enlarged and similarly replaced by thin-walled unilocular cysts of variable sizes. The inner surface is smooth. No solid areas, papillary excrescences or bile staining seen.
(Bottom) Pancreas: The enlarged organ is a mass of similar thin-walled cysts which would have been filled with clear serous fluid.